EWING’S SARCOMA OF MANDIBLE: A RARE TUMOR AT A RARE LOCATION

Abstract

Ewing’s Sarcoma (ES) is a rare, highly malignant, and a poorly differentiated variant of round small cell tumors with the most unfavorable prognosis among all musculoskeletal neoplasms. The histogenesis of ES is still uncertain. However, the latest studies suggest it to be neural crest progenitor cell-derived or neuroectodermally originated primitive neural tissue with various degrees of differentiation [1, 2]. It is an uncommon malignancy of bones (rarely soft tissue) and usually occurs in long bones of children and young adults. ES rarely occurs in the skull (2.3%). But when it does, maxilla and mandible are its usual primary locations [3]. In this case report, we have presented a rare case of a 4-years old girl with ES of the mandible whichwas precisely diagnosed and effectively treated using a multi-disciplinary approach. This study aims to spread awareness among physicians to rule out the chances of malignancy in a rapidly growing dental or facial swelling. It also underscores the potential of a better prognosis by timely diagnosing and promptly managing Ewing’s Sarcoma in children.