A Case of Congenitally Corrected Transposition of Great Arteries Presented with Intracardiac Anomelies and Situs Inversus in a 28 year Old Male: A Rare Case Report

Abstract

Congenitally corrected transposition of the great arteries (CCTGA) Situs inversus with levocardia represents a relatively very rare congenital condition and most patients are diagnosed in infancy or early age. Congenitally corrected transposition of the great arteries (CCTGA) accounts for less than1% of cardiac anomalies, and is defined as ventriculoarterial and atrioventricular (AV) discordance. The double discordant connection allows for survival with the right ventricle performing as the systemic ventricle, and the left ventricle as the pulmonary ventricle. we reported a case of 28year old male with congenitally corrected transposition of the great arteries which presented with 9month history of exertional dyspnea. A diagnosis was confirmed by echocardiogram showing situs inversus, levocardia, atrioventricular and ventriculoarterial discordance, VSD with bidirectional flow and sever pulmonary stenosis. Surgical intervention not done due to higher risk of anatomic repair. Although management of the corrected transposition of the great arteries patients remains controversial, the recommendation is that physiologic repair may be the procedure of choice for some patients particularly complicated cases. anatomic repair is not always suitable for older patients.

Keywords: Congenitally Corrected, Levocardia, Situs Inversus